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Total anomalous pulmonary venous return



Cardiovascular system


Vascular disorders
Congenital heart defects
Cardiac arrhythmias
Valvular disorders
Heart failure
Cardiac infections
Pericardial disorders
Cardiac tumors
Cardiovascular system pathology review

Total anomalous pulmonary venous return


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High Yield Notes
12 pages

Total anomalous pulmonary venous return

2 flashcards

USMLE® Step 1 style questions USMLE

1 questions

A 2-day-old male newborn is being evaluated in the neonatal intensive care unit for progressive cyanosis, breathing difficulty and poor feeding. He was born to a 22-year-old mother who received no prenatal care. Temperature is 37.0° C (98.6° F), pulse is 160/min, blood pressure is 87/55 mm Hg, and respiration rate is 55/min. On physical examination, no craniofacial deformities are seen. Central cyanosis is present, and cardiac auscultation reveals fixed splitting of the second heart sound (S2) over the left upper sternal border. Chest radiograph is obtained and shown below:  

Reproduced from: Radiopaedia    
Which of the following is the most likely diagnosis?  

Anomalous pulmonary venous connection is a rare cyanotic congenital heart defect in which all four pulmonary veins are malpositioned and make anomalous connections to the systemic venous circulation. Normally, pulmonary veins return oxygenated blood from the lungs to the left atrium where it can then be pumped to the rest of the body. A patent foramen ovale, patent ductus arteriosa or an atrial septal defect must be present, or else the condition is fatal due to a lack of systemic blood flow.