Dubin-Johnson syndrome presents with (conjugated/unconjugated) hyperbilirubinemia.
USMLE® Step 1 style questions USMLE
USMLE® Step 2 style questions USMLE
A 5-month-old infant comes for an office visit. Laboratory results show congenital hyperbilirubinemia. AST and ALT concentrations are normal, and his coproporphyrin I to coproporphyrin III ratio is greatly increased. A liver biopsy shows a dark green macroscopic specimen. Which of the following is the most likely diagnosis?