Bernard-Soulier syndrome
Bernard-Soulier syndrome
Heme & Onc
Heme & Onc
Blood groups and transfusions
Platelet plug formation (primary hemostasis)
Coagulation (secondary hemostasis)
Role of Vitamin K in coagulation
Clot retraction and fibrinolysis
Hemophilia
Vitamin K deficiency
Bernard-Soulier syndrome
Glanzmann's thrombasthenia
Hemolytic-uremic syndrome
Immune thrombocytopenia
Thrombotic thrombocytopenic purpura
Von Willebrand disease
Disseminated intravascular coagulation
Heparin-induced thrombocytopenia
Antithrombin III deficiency
Factor V Leiden
Protein C deficiency
Protein S deficiency
Antiphospholipid syndrome
Anticoagulants: Heparin
Anticoagulants: Warfarin
Anticoagulants: Direct factor inhibitors
Antiplatelet medications
Thrombolytics
Blood histology
Erythropoietin
Iron deficiency anemia
Anemia of chronic disease
Sideroblastic anemia
Megaloblastic anemia
Aplastic anemia
Paroxysmal nocturnal hemoglobinuria
Autoimmune hemolytic anemia
Fanconi anemia
Hemolytic disease of the newborn
Hereditary spherocytosis
Glucose-6-phosphate dehydrogenase (G6PD) deficiency
Pyruvate kinase deficiency
Sickle cell disease (NORD)
Beta-thalassemia
Alpha-thalassemia
Lead poisoning
Folate (Vitamin B9) deficiency
Vitamin B12 deficiency
Diamond-Blackfan anemia
Acute intermittent porphyria
Porphyria cutanea tarda
Hodgkin lymphoma
Non-Hodgkin lymphoma
Chronic leukemia
Acute leukemia
Myelodysplastic syndromes
Polycythemia vera (NORD)
Myelofibrosis (NORD)
Essential thrombocythemia (NORD)
Langerhans cell histiocytosis
Mastocytosis (NORD)
Multiple myeloma
Monoclonal gammopathy of undetermined significance
Waldenstrom macroglobulinemia
Leukemoid reaction
Microcytic anemia: Pathology review
Non-hemolytic normocytic anemia: Pathology review
Intrinsic hemolytic normocytic anemia: Pathology review
Extrinsic hemolytic normocytic anemia: Pathology review
Macrocytic anemia: Pathology review
Heme synthesis disorders: Pathology review
Coagulation disorders: Pathology review
Platelet disorders: Pathology review
Mixed platelet and coagulation disorders: Pathology review
Thrombosis syndromes (hypercoagulability): Pathology review
Lymphomas: Pathology review
Leukemias: Pathology review
Plasma cell disorders: Pathology review
Myeloproliferative disorders: Pathology review
Hematopoietic medications
Ribonucleotide reductase inhibitors
Topoisomerase inhibitors
Platinum containing medications
Anti-tumor antibiotics
Microtubule inhibitors
DNA alkylating medications
Monoclonal antibodies
Antimetabolites for cancer treatment
Ehrlichia and Anaplasma
Escherichia coli
Rickettsia rickettsii (Rocky Mountain spotted fever) and other Rickettsia species
Plasmodium species (Malaria)
HIV (AIDS)
HIV and AIDS: Pathology review
Measles virus
Viral hepatitis: Pathology review
Viral hepatitis
Hepatitis C virus
Hepatitis medications
Dengue virus
Yellow fever virus
Cytomegalovirus
Epstein-Barr virus (Infectious mononucleosis)
Bleeding disorders: Clinical
Clostridium perfringens
Staphylococcus epidermidis
Staphylococcus aureus
Streptococcus pneumoniae
Streptococcus pyogenes (Group A Strep)
Enterococcus
Salmonella (non-typhoidal)
Salmonella typhi (typhoid fever)
Pseudomonas aeruginosa
Serratia marcescens
Nocardia
Klebsiella pneumoniae
Legionella pneumophila (Legionnaires disease and Pontiac fever)
Neisseria meningitidis
Brucella
Haemophilus influenzae
Mycobacterium avium complex (NORD)
Mycobacterium tuberculosis (Tuberculosis)
Mycoplasma pneumoniae
Borrelia species (Relapsing fever)
Borrelia burgdorferi (Lyme disease)
Varicella zoster virus
Human herpesvirus 8 (Kaposi sarcoma)
Herpes simplex virus
Adenovirus
Parvovirus B19
Human papillomavirus
JC virus (Progressive multifocal leukoencephalopathy)
Human T-lymphotropic virus
Candida
Pneumocystis jirovecii (Pneumocystis pneumonia)
Coccidioidomycosis and paracoccidioidomycosis
Histoplasmosis
Aspergillus fumigatus
Mucormycosis
Cryptococcus neoformans
Babesia
Cryptosporidium
Toxoplasma gondii (Toxoplasmosis)
Leishmania
Strongyloides stercoralis
Diphyllobothrium latum
Ancylostoma duodenale and Necator americanus
Key Takeaways
Bernard-Soulier syndrome (BSS) is a rare congenital bleeding disorder characterized by thrombocytopenia, unusually giant platelets, and prolonged bleeding time. Patients with BSS typically have prolonged or severe bleeding after minor trauma or surgery and may also develop epistaxis, hematomas, and petechiae. The severity of the condition can vary from mild to life-threatening.