Cleft lip and palate: Nursing

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Cleft lip and palate: Nursing

Nicu

Nicu

Respiratory stimulants: Nursing pharmacology
Immunoglobulins: Nursing pharmacology
Neonatal eye prophylaxis: Nursing pharmacology
Phytonadione (Vitamin K1): Nursing pharmacology
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Fetal circulation: Nursing
Shoulder dystocia: Nursing
Brachial plexus injury: Nursing
Newborn adaptation to extrauterine life: Nursing
Growth and development - Infant: Nursing
Assessment of gestational age: Nursing
Small for gestational age (SGA) infant: Nursing
Large for gestational age (LGA) infant: Nursing
Preterm infant: Nursing
Postterm infant: Nursing
Nutrition - Newborn: Nursing
Physiology of lactation: Nursing
Physical assessment - Neonate: Nursing
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Thermoregulation - Neonate: Nursing
Neonatal sepsis: Nursing
Biliary atresia: Nursing
Esophageal atresia and tracheoesophageal fistula: Nursing
Cleft lip and palate: Nursing
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Group B streptococcus (GBS) infection in pregnancy: Nursing

Notes

CLEFT LIP AND PALATE

KEY POINTS
NOTES
DEFINITION
  • Cleft lip
    • Opening or split in the upper lip
  • Cleft palate
    • Opening or split in the hard palate

PHYSIOLOGY
  • Upper lip
    • Maxillary prominences grow medially to fuse with medial nasal placodes
  • Hard palate
    • Medial nasal placodes grow inside the face giving rise to anterior portion
    • Palatal shelves fuse above the tongue remaining portion

CAUSES AND RISK FACTORS
  • Causes
    • Unkown
  • Risk factors
    • Folate deficiency
    • Maternal smoking
    • Exposure to radiation
    • Certain medications
    • Advanced maternal age
    • Certain infections during pregnancy

PATHOPHYSIOLOGY
  • Cleft lip
    • Maxillary prominences fail to fuse with medial nasal prominences at midline 
  • Cleft palate
    • Palatal shelves fail to fuse at midline
  • Complications
    • Feeding difficulties
    • Altered dentition
    • Delayed or altered speech
    • Recurrent otitis media

SIGNS AND SYMPTOMS
  • Split in upper lip and/or roof of mouth

DIAGNOSIS
  • Physical assessment
  • Prenatal ultrasound

TREATMENT
  • Surgery

MANAGEMENT OF CARE
  • Goals of care
    • Provide postoperative care
    • Provide emotional support
  • Implement routine postoperative interventions
  • Apply elbow immobilizers
  • Maintain Logan bow
  • Provide small feedings
  • Position upright following feedings
  • Rinse mouth 
  • Encourage caregivers to participate in care
  • Use active listening
  • Allow time to ask questions
  • Provide clear, concise answers

PATIENT AND FAMILY TEACHING
  • Explain condition, plan of care, and how to safely administer medications
  • Keep all follow-up appointments
  • Instruct how to feed with a syringe
  • Teach how to care for incision site 
  • Reinforce keeping elbow restraints in place
  • Notify HCP
    • Redness
    • Swelling
    • Bleeding
    • Bad-smelling drainage
    • Increased pain

Transcript

Watch video only

Cleft lip is an opening or a split in the upper lip, whereas cleft palate describes an opening or a split in the roof of the mouth, called the hard palate. Cleft lip and palate are the most common congenital anomalies of the head and face.

Now, let’s quickly review the embryological development of the lips and palate. At the fourth week of pregnancy, multiple structures appear in the face of the embryo. These include the frontonasal prominence, which gives rise to the forehead and bridge of the nose; nasal placodes, which are two raised bumps on each side of the frontonasal prominence; as well as paired maxillary prominences; and paired mandibular prominences. Additionally, two small dimples develop at the center of each nasal placode, dividing these placodes into medial and lateral nasal prominences.

Now let’s look at a cross section of the embryo. As the embryo develops, the maxillary prominences grow medially to fuse with the medial nasal placodes, giving rise to the upper lip. In addition, the medial nasal placodes grow to the inside of the face, forming the intermaxillary segment, which later on forms the anterior one third of the hard palate, called the primary palate. Similarly, the maxillary prominences grow to the inside of the face, forming the palatal shelves. These shelves will then fuse above the tongue to form the remaining two thirds of the hard palate, called the secondary palate.

Alright, now the cause of cleft lip and palate is unknown, with some theories suggesting multifactorial genetic and environmental involvement. However, several risk factors for cleft lip and palate have been identified, including folate deficiency, as well as exposure to teratogens, such as maternal smoking and exposure to radiation, and using certain medications during pregnancy, such as anticonvulsants or steroids. Other risk factors include advanced maternal age, and certain infections during pregnancy, especially the rubella virus.

Moving on to pathology and starting with cleft lip, the maxillary prominences fail to fuse with the medial nasal prominences at the midline, causing a split in the upper lip. On the other hand, a cleft palate occurs when the palatal shelves fail to fuse at the midline.

When it comes to complications of cleft lip and palate, these include feeding difficulties, which can lead to insufficient growth; as well as altered dentition; delayed or altered speech development; and recurrent otitis media that can progress to hearing loss. Other complications are often caused by a cleft palate, and these include gagging, choking, and nasal regurgitation of milk.

Clients with cleft lip and palate typically present with a split in the upper lip or a split in the roof of the mouth. A cleft lip can present without a cleft palate, and vice versa, with up to 50 percent of clients presenting with both defects. These defects can be bilateral, meaning on both sides, or unilateral, meaning on one side only, with the left side being more commonly affected. Other signs and symptoms include a split in the upper lip that extends to one or both nostrils; or a split in the hard palate that doesn’t affect the face.

The diagnosis of cleft lip and palate is based on physical assessment of the newborn, and can also be done prenatally via routine ultrasound.

The mainstay of treating cleft lip and palate is surgery, which aims at improving the child’s ability to eat, speak, and hear normally, in addition to restoring normal facial appearance. Surgical repair of cleft lip, or cheiloplasty, usually occurs between 3 and 6 months of age. Surgical repair of cleft palate, or palatoplasty, is corrected with a series of surgeries. The initial surgery usually occurs between 6 and 12 months of age.

Alright, now let’s look at the nursing care you’ll provide to an infant with a cleft lip. Your primary nursing goals are to provide postoperative care and provide emotional support.

Okay, begin by implementing routine postoperative interventions, and monitor the infant closely for complications related to the procedure. To help decrease the risk of damaging the surgical site, apply soft elbow immobilizers that allow movement, but prevent the infant from bending their arm at the elbow to reach the suture line. Also maintain the curved metal protective device called a Logan bow, to provide additional protection and to decrease stress on the surgical site.

Sources

  1. "Medical-Surgical Nursing" Elsevier (2020)
  2. "Lewis's Medical-Surgical Nursing" Mosby (2019)
  3. "Saunders Comprehensive Review for the NCLEX-RN Examination" Saunders (2016)
  4. "Maternal Child Nursing Care" Elsevier Health Sciences (2014)
  5. "Essentials of Pediatric Nursing" LWW (2020)
  6. "Prenatal diagnosis of cleft lip and cleft lip palate – a case series" Medical Ultrasonography (2018)
  7. "State-Mandated Coverage of Cleft Lip and Cleft Palate Treatment" The Cleft Palate-Craniofacial Journal (2020)
  8. "Regulatory Mechanisms of Soft Palate Development and Malformations" Journal of Dental Research (2019)
  9. "Cleft lip and palate: Care configuration, national registration, and research strategies" Journal of the World Federation of Orthodontists (2020)