Glanzmann's thrombasthenia

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Glanzmann's thrombasthenia

After Daily Test

After Daily Test

Hypokalemia: Clinical
Pharyngeal arches, pouches, and clefts
Cluster A personality disorders
Carpal tunnel syndrome
Hypoglycemics: Insulin secretagogues
Endometriosis
Pemphigus vulgaris
Dandy-Walker malformation
Sturge-Weber syndrome
Hypersensitivity skin reactions: Clinical
Cirrhosis: Clinical
Thrombocytopenia: Clinical
Osteomalacia
Ovarian cysts, cancer, and other adnexal masses: Clinical
Muscular dystrophy
Neurofibromatosis
Syncope: Clinical
Dermatomyositis
Postpartum hemorrhage
Chronic granulomatous disease
Rhabdomyolysis
Mitochondrial myopathy
Sarcoidosis
Edwards syndrome (Trisomy 18)
Ulcerative colitis
Achondroplasia
Systemic lupus erythematosus
Sleep
Sleep disorders: Clinical
Anti-tumor antibiotics
Female reproductive system: Reproductive system disorders
Cyanide poisoning
Malassezia (Tinea versicolor and Seborrhoeic dermatitis)
Seizures: Clinical
Bullous pemphigoid
Cardiac and vascular tumors: Pathology review
Meckel diverticulum
Psychomotor stimulants
Narcolepsy (NORD)
Patau syndrome (Trisomy 13)
Osteochondroma
Nocardia
Polycythemia vera (NORD)
Pleural effusion
Toxidromes: Clinical
Syringomyelia
Alzheimer disease
Lung cancer
Diamond-Blackfan anemia
Chronic pyelonephritis
Gestational trophoblastic disease
Vestibulo-ocular reflex and nystagmus
Wiskott-Aldrich syndrome
Insomnia
Rubella virus
Anticoagulants: Warfarin
Periorbital cellulitis
Naegleria fowleri (Primary amebic meningoencephalitis)
Gardnerella vaginalis (Bacterial vaginosis)
Congenital diaphragmatic hernia
Acute leukemia
Hemochromatosis
Glanzmann's thrombasthenia
Nervous system: Brain and spinal cord injuries
Ovarian torsion
Mallory-Weiss syndrome
Hyperthyroidism medications
Fibrocystic breast changes
Miscellaneous antifungal medications
Reactive arthritis
Prostatitis
Pressure ulcer
Hashimoto thyroiditis
Subdural hematoma
Metachromatic leukodystrophy (NORD)
Compartment syndrome
Pediatric infectious rashes: Clinical
Fetal alcohol syndrome
Haemophilus ducreyi (Chancroid)
Amenorrhea: Clinical
Polycystic ovary syndrome
Neuroleptic malignant syndrome
Development of the fetal membranes
Anti-parkinson medications

Key Takeaways

Glanzmann's thrombasthenia is a rare autosomal recessive bleeding disorder caused by defects in platelet aggregation. In Glanzmann's thrombasthenia, platelets are deficient in the fibrinogen receptor GpIIb/IIIa necessary for proper platelet aggregation. This leads to easy bruising, mucosa bleeding, and prolonged bleeding from even minor cuts. It can also cause internal bleeding, which can be life-threatening.