Summary of Prions (Spongiform encephalopathy)
Flashcards on Prions (Spongiform encephalopathy)
Prions (Spongiform encephalopathy)
encephalopathy is characterized by dementia, ataxia and death.
Questions on Prions (Spongiform encephalopathy)
Transmissible spongiform encephalopathy
A 50-year-old man of Italian descent comes to the clinic because of progressively worsening insomnia. He has also experienced rapidly progressive changes in his mental status and behavior, including inattention, impaired concentration, and confusion. The patient also reports feeling in a dream-like state during his waking hours, and has had hallucinations. He is hypertensive, tachycardic and hyperthermic. On physical examination, the patient is sweating excessively. A sleep study is performed to assess his insomnia. The patient's sleep study demonstrates an inability to progress beyond Stage 1 sleep. Which of the following is the most likely diagnosis?